Urol. praxi. 2023;24(3):177-179 | DOI: 10.36290/uro.2023.069

Metastatic/multicentric renal epithelioid angiomyolipoma - clinical case report

MUDr. Ondřej Cempírek1, MUDr. Tomáš Málek1, MUDr. Roman Boháč2
1 Urologické oddělení, Nemocnice Havlíčkův Brod, p. o.
2 Patologické oddělení, Nemocnice Havlíčkův Brod, p. o.

Renal epithelioid angiomyolipoma (ReAML) is a rare subtype of angiomyolipoma. It is a benign kidney disease, in which cases of aggressive behavior and malignancy have been reported. These tumors represent 8% of operated kidney angiomyolipomas. Diagnosis is based on histological findings. The aim of this text is to review the information on this issue, the histological picture and the case report of a 42-year-old woman operated at our department who was found to have multicentric or metastatic involvement of the retroperitoneal lymph node.

Keywords: renal epithelioid angiomyolipoma, PECom, cathepsin K, mTOR.

Accepted: September 25, 2023; Published: October 2, 2023  Show citation

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Cempírek O, Málek T, Boháč R. Metastatic/multicentric renal epithelioid angiomyolipoma - clinical case report. Urol. praxi. 2023;24(3):177-179. doi: 10.36290/uro.2023.069.
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